Autoimmune Hepatitis with Distal Renal Tubular Acidosis
and Small Bowel Partial Malrotation

Akash Shukla; Tejas Kanaiyalal Modi; Hardik Parikh; Abhishek Sadalge; Amit Gupte; Pratin Bhatt

doi:10.5005/jp-journals-10018-1145

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Autoimmune Hepatitis with Distal Renal Tubular Acidosis and Small Bowel Partial Malrotation

Akash Shukla, Tejas Kanaiyalal Modi, Hardik Parikh, Abhishek Sadalge, Amit Gupte, Pratin Bhatt

Citation Information : Shukla A, Kanaiyalal Modi T, Parikh H, Sadalge A, Gupte A, Bhatt P. Autoimmune Hepatitis with Distal Renal Tubular Acidosis and Small Bowel Partial Malrotation. Euroasian J Hepatogastroenterol 2015; 5 (2):107-109.

DOI: 10.5005/jp-journals-10018-1145

License: CC BY-NC 4.0

Published Online: 01-06-2017

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Abstract

Renal tubular acidosis (RTA) is not uncommon in patient with chronic autoimmune hepatitis (AIH), but usually remains latent. Here, we report a case of renal tubular acidosis RTA who presented with AIH. She was also diagnosed to have partial bowel malrotation. A 9-year-old girl, a case of distal RTA, presented with jaundice, abdominal distension and altered sensorium. She was diagnosed to be AIH, which was successfully treated with steroids and azathioprine. Coexistent midgut partial malrotation with volvulus was diagnosed during the treatment. She was treated successfully with anti-tuberculous treatment for cervical lymphadenitis. Autoimmune hepatitis should not be ruled out in each case of RTA presenting with jaundice.

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