Low Grade Appendiceal Mucinous Neoplasm with
Pseudomyxoma Peritonei: An Enigma for Pathologist
Veena Maheshwari, Kiran Alam, Nishat Afroz, Feroz Alam
Citation Information :
Maheshwari V, Alam K, Afroz N, Alam F. Low Grade Appendiceal Mucinous Neoplasm with Pseudomyxoma Peritonei: An Enigma for Pathologist. Euroasian J Hepatogastroenterol 2014; 4 (2):113-116.
Malignant mucinous neoplasms of the appendix is an infrequently encountered entity. Extraappendiceal
spread of these tumor is one of the commonest etiology of pseudomyxoma peritonei,
which demands a hightened vigilance in their early diagnosis. Although low-grade appendiceal
mucinous neoplasms (LAMNs) largely stay confined to the appendix, but they can spread to the
peritoneum as pseudomyxoma peritonei leading to an unpredictable outcome. Due to the rare
occurrence of low-grade appendiceal neoplasm only tenuous and limited information is present in
the medical literature. We report a case of LAMN with pseudomyxoma peritonei in a 45-year-old
male, who presented with the complaints of abdominal distension associated with abdominal pain
and constipation. Clinical examinations and computed tomography (CT) scan were suggestive of
pseudomyxoma peritonei. Peroperative findings and histopathological examination rendered a
conclusive diagnosis of low-grade appendiceal neoplasm.
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