Euroasian journal of hepato-gastroenterology

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VOLUME 4 , ISSUE 2 ( July-December, 2014 ) > List of Articles


Low Grade Appendiceal Mucinous Neoplasm with Pseudomyxoma Peritonei: An Enigma for Pathologist

Veena Maheshwari, Kiran Alam, Nishat Afroz, Feroz Alam

Citation Information : Maheshwari V, Alam K, Afroz N, Alam F. Low Grade Appendiceal Mucinous Neoplasm with Pseudomyxoma Peritonei: An Enigma for Pathologist. Euroasian J Hepatogastroenterol 2014; 4 (2):113-116.

DOI: 10.5005/jp-journals-10018-1115

License: CC BY-NC 4.0

Published Online: 01-01-2014

Copyright Statement:  Copyright © 2014; The Author(s).


Malignant mucinous neoplasms of the appendix is an infrequently encountered entity. Extraappendiceal spread of these tumor is one of the commonest etiology of pseudomyxoma peritonei, which demands a hightened vigilance in their early diagnosis. Although low-grade appendiceal mucinous neoplasms (LAMNs) largely stay confined to the appendix, but they can spread to the peritoneum as pseudomyxoma peritonei leading to an unpredictable outcome. Due to the rare occurrence of low-grade appendiceal neoplasm only tenuous and limited information is present in the medical literature. We report a case of LAMN with pseudomyxoma peritonei in a 45-year-old male, who presented with the complaints of abdominal distension associated with abdominal pain and constipation. Clinical examinations and computed tomography (CT) scan were suggestive of pseudomyxoma peritonei. Peroperative findings and histopathological examination rendered a conclusive diagnosis of low-grade appendiceal neoplasm.

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