A Female with Benign Recurrent Intrahepatic Cholestasis
Swapan Chandra Dhar, Chanchal Kumar Ghosh, Sasanka Kumar Saha, Nikhil Chandra Nath, Helal Uddin, Mohammad Wareshuzzaman, Mohammad Omar Faruk
Citation Information :
Chandra Dhar S, Kumar Ghosh C, Kumar Saha S, Chandra Nath N, Uddin H, Wareshuzzaman M, Omar Faruk M. A Female with Benign Recurrent Intrahepatic Cholestasis. Euroasian J Hepatogastroenterol 2012; 2 (2):113-115.
Benign recurrent intrahepatic cholestasis (BRIC) is a rare
autosomal recessive or sporadic disorder, characterized by
recurrent episodes of intense pruritus and jaundice that resolve
spontaneously without any residual liver damage. Episodic
attack can occur at any age but is usually seen at 2nd decade
of life. We here report a young female with BRIC who presented
the recurrent attack of cholestatic jaundice and pruritus, but
was negative for all possible etiology. Liver biopsy was consistent
with intrahepatic cholestasis. She was improved after 3 months
of suffering from jaundice. On follow-up, she was alright after
attack.
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