Euroasian journal of hepato-gastroenterology

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VOLUME 10 , ISSUE 1 ( January-June, 2020 ) > List of Articles


Benign Hepatic Nodules Mimicking Hepatocellular Carcinoma in the Setting of Fontan-associated Liver Disease: A Case Report

Anıl Çolaklar, Stephen J Lehnert, Temel Tirkes

Keywords : Congenital heart disease, Fontan procedure, Imaging features, Liver lesion

Citation Information : Çolaklar A, Lehnert SJ, Tirkes T. Benign Hepatic Nodules Mimicking Hepatocellular Carcinoma in the Setting of Fontan-associated Liver Disease: A Case Report. Euroasian J Hepatogastroenterol 2020; 10 (1):42-44.

DOI: 10.5005/jp-journals-10018-1315

License: CC BY-NC 4.0

Published Online: 22-08-2020

Copyright Statement:  Copyright © 2020; The Author(s).


Fontan procedure, in which systemic circulation is redirected into pulmonary circulation by a baffle, is a palliative surgical strategy for patients born with single ventricle congenital heart disease. Hemodynamic changes secondary to Fontan procedure, also termed as Fontan physiology, result in end-organ damage, especially of the liver. Fontan-associated liver disease (FALD) represents a spectrum of pathologies ranging from mild liver fibrosis to advanced liver cirrhosis and hepatocellular carcinoma (HCC). Hepatic nodules, some of which have been documented as HCC in several case series and reports, are a recognized complicated feature of FALD. Herein, we report a case with benign hepatic nodules mimicking HCC by imaging characteristics, emphasizing the fact that arterially enhancing lesions with delayed washout appearance may reflect benign regenerative or focal nodular hyperplasia-like nodules in patients with Fontan physiology.

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